An Oral Clinician’s Perspective towards Peutz Jegher’s Syndrome – A Case Report
نویسنده
چکیده
Peutz Jegher’s syndrome is a mucocutaneous autosomal dominant condition associated with extensive melanin pigmentation and intestinal hamartomatous polyp formation. It is characterised by round, oval patches of blackish brown pigmentation, irregularly distributed over the oral mucosa, lips, tongue and the hard palate. This condition is associated with an increased risk towards carcinoma and several other complications like small intestine intussusception and anemia. The current case report highlights the oral manifestations of Peutz Jeghers syndrome; also it enumerates the important role played by an oral clinician in the early diagnosis of this inherited syndrome, thereby reducing the morbidity.
منابع مشابه
Peutz Jeghers syndrome (gastro-intestinal polyposis) and its complications.
A rare case of multiple jejunal poiyps, presenting as an acute abdominal emergency with complications of mtussusception and gangrene is discussed. The relevant features of Peutz Jegher’s syndrome and the surgical management of it’s complications are highlighted (JPMA 35 : 154, 1985).
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